Test Code SAU Sialic Acid, Free and Total, Random, Urine
Ordering Guidance
This is a recommended screening test for patients suspected to have a diagnosis of free sialic acid storage disease.
Urine oligosaccharides are also recommended for patients with a suspected diagnosis of sialidosis or galactosialidosis.
Necessary Information
Patient's age is required.
Specimen Required
Supplies: Sarstedt 5 mL Aliquot Tube (T914)
Container/Tube: Plastic, 5-mL urine tube
Specimen Volume: 1 mL
Pediatric Volume: 0.5 mL
Collection Instructions: Collect a random urine specimen (early morning preferred).
Forms
1. Biochemical Genetics Patient Information (T602)
2. If not ordering electronically, complete, print, and send a Biochemical Genetics Test Request (T798) with the specimen.
Useful For
Screening for sialic acid disorders
Special Instructions
Method Name
Liquid Chromatography Tandem Mass Spectrometry (LC-MS/MS)
Reporting Name
Sialic Acid, Free and Total, USpecimen Type
UrineSpecimen Minimum Volume
0.5 mL
Specimen Stability Information
Specimen Type | Temperature | Time | Special Container |
---|---|---|---|
Urine | Refrigerated (preferred) | 90 days | |
Frozen | 90 days |
Reference Values
Free Sialic Acid:
≤4 weeks: ≤208 mmol/mol creatinine
5 weeks-12 months: ≤104 mmol/mol creatinine
13 months-18 years: ≤100 mmol/mol creatinine
≥19 years: ≤38 mmol/mol creatinine
Total Sialic Acid
≤4 weeks: ≤852 mmol/mol creatinine
5 weeks-12 months: ≤656 mmol/mol creatinine
13 months-18 years: ≤335 mmol/mol creatinine
≥19 years: ≤262 mmol/mol creatinine
Total/Free Ratio:
≤4 weeks: 1.94-18.68
5 weeks-12 months: 2.34-13.85
13 months-18 years: 2.63-9.18
≥19 years: 3.35-15.81
An interpretive report will also be provided.
Day(s) Performed
Friday
Report Available
5 to 11 daysPerforming Laboratory
Mayo Clinic Laboratories in RochesterTest Classification
This test was developed and its performance characteristics determined by Mayo Clinic in a manner consistent with CLIA requirements. It has not been cleared or approved by the US Food and Drug Administration.CPT Code Information
84275
LOINC Code Information
Test ID | Test Order Name | Order LOINC Value |
---|---|---|
SAU | Sialic Acid, Free and Total, U | 104657-2 |
Result ID | Test Result Name | Result LOINC Value |
---|---|---|
621069 | Free Sialic Acid | 104658-0 |
621070 | Total Sialic Acid | 104659-8 |
621071 | Total/Free Sialic Acid Ratio | 104660-6 |
621072 | Interpretation | 94423-1 |
621073 | Reviewed By | 18771-6 |